Alpha galactosidase A抗体-抗体-抗体-生物在线
上海信裕生物科技有限公司
Alpha galactosidase A抗体

Alpha galactosidase A抗体

商家询价

产品名称: Alpha galactosidase A抗体

英文名称: Alpha galactosidase AAntibody

产品编号: XY15428-1

产品价格: null

产品产地: 中国/美国

品牌商标: XYbscience

更新时间: 2023-08-17T09:55:27

使用范围: WB,ELISA,IHC-P,IHC-F,IF

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 ALPHA GALACTOSIDASE A抗体

Applications
In-house applications ELISA, IHC, IP, WB     Application not tested? Please see our Guarantee.
Species specificity Human,Mouse,Rat; other species not tested.
Images
Prev12NextView more validation data
  • 15428-1-AP;HeLa cellsHeLa cells were subjected to SDS PAGE followed by western blot with 15428-1-AP(GLA antibody) at dilution of 1:1000
  • 15428-1-AP;H-liverImmunohistochemical of paraffin-embedded human liver using 15428-1-AP(GLA antibody) at dilution of 1:50 (under 10x lens)
  • 15428-1-AP;H-liverImmunohistochemical of paraffin-embedded human liver using 15428-1-AP(GLA antibody) at dilution of 1:50 (under 40x lens)
  • 15428-1-AP;HEK-293 cellsIP Result of anti-GLA (IP:15428-1-AP, 3ug; Detection:15428-1-AP 1:1000) with HEK-293 cells lysate 1800ug.
Positive WB detected in HeLa cells, HEK-293 cells
Positive IP detected in HEK-293 cells
Positive IHC detected in Human liver tissue, human liver cancer tissue, mouse liver tissue
Recommended dilution WB : 1:500-1:5000
IP : 1:500-1:5000
IHC : 1:20-1:200
 ALPHA GALACTOSIDASE A抗体Application key: WB = Western blotting, IHC = Immunohistochemistry, IF = Immunofluorescence,
IP = Immunoprecipitation
Product Information
Source Rabbit Purification method Antigen affinity purification
Isotype IgG Storage PBS with 0.02% sodium azide and 50% glycerol pH 7.3. Store at -20oC.
Immunogen Information
Immunogen Alpha galactosidase A fusion protein ag7609 Full name Galactosidase, alpha
Calculated molecular
weight
49 kDa Observed molecular 
weight
49 kDa
GenBank accession 
number
BC002689 Gene ID (NCBI) 2717
Gene symbol GLA Synonyms Alpha galactosidase A, galactosidase, alpha
Background ALPHA GALACTOSIDASE A抗体

GLA, also named as Melibiase, Agalsidas and Alpha-galactosidase A, Belongs to the glycosyl hydrolase 27 family. It hydrolysis of terminal, non-reducing alpha-D-galactose residues in alpha-D-galactosides, including galactose oligosaccharides, galactomannans and galactolipids. Fabry disease is an X-linked lysosomal storage disorder resulting from the deficient activity of GLA. Enzyme replacement therapy (ERT) with GLA is currently the most effective therapeutic strategy for patients with Fabry disease, a lysosomal storage disease. ALPHA GALACTOSIDASE A抗体

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